Dentinogenesis Imperfecta is "An autosomal dominant disorder of tooth development characterized by opalescent dentin resulting in discoloration of the teeth, ranging from dusky blue to brownish. The dentin is poorly formed with an abnormally low mineral content; the pulp canal is obliterated, but the enamel is normal. The teeth usually wear down rapidly, leaving short, brown stumps". Clinical features are opalescent teeth, under-mineralized dentin, bulb-shaped crowns with constricted cementoenamel junctions and thin roots. Teeth fracture and chip away easily leading to exposed dentin and attrition. Histological features are disoriented, irregular, widely spaced dentinal tubules. There is calcification of pulp canals with cellular inclusions. Treatment comporises of composite resin restorations, laminate veneers, stainless steel crowns on the molars, and overdentures depends upon amount of tooth destruction. Prognosis is good if diagnosed early. A case of dentingenesis Imperfecta is presented along with problems in the management of this condition. These problems may not arise if diagnose the patient at early stage and start the treatment. CONCLUSIONS: A thorough family history and a proper clinical evaluation is necessary to diagnose dentinogenesis Imperfecta.