Total Cavopulmonary Connection for Functionally Single Ventricle without Cardiopulmonary Bypass Support.

Sohail Khan Bangash; Iqbal Hussain Pathan; Saad Bader Zaki

Author(s)

Sohail Khan Bangash Department of Paediatric Cardiac Surgery, National Institute of Cardiovascular Diseases (NICVD), Karachi, Pakistan

Iqbal Hussain Pathan Department of Paediatric Cardiac Surgery, National Institute of Cardiovascular Diseases (NICVD), Karachi, Pakistan

Saad Bader Zaki Department of Paediatric Cardiac Surgery, National Institute of Cardiovascular Diseases (NICVD), Karachi, Pakistan

Abstract

A heart with two atriums but one ventricle, an anatomy with a unique physiology, is responsible for many creative surgical and interventional approaches in history. Different surgical techniques have been used to address this strange physiology of parallel circulation. All these attempts met with failure till the concept of Fontan circulation was described. Currently, controversy exists between multistage vs. single stage total cavopulmonary connections. Total cavopulmonary connection is the only definitive procedure performed to provide palliation for patients with complex congenital heart defects which cannot support a biventricular circulation. We report a case with tricuspid atresia with transposition of great arteries and pulmonary stenosis with persistant left-sided superior vena cava and functionally single ventricle. Patient successfully underwent single stage extra-cardiac total cavopulmonary connection. In this case, bilateral Glenn with extra-cardiac inferior vena cava to main pulmonary artery shunt was performed off-pump.

Publication Details

Page(s) 855-857

DOI DOI not available

Published Journal: Journal of College of Physicians and Surgeons--Pakistan : JCPSP, Volume: 26, Issue: 10, Year: 2016

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