Spindle Cell Sarcoma Presenting as Pancoast Syndrome.

Aliena Badshah; Salman Khan; Usman Saeed

Author(s)

Aliena Badshah Department of Medicine, Khyber Teaching Hospital, Peshawar, Pakistan

Salman Khan Department of Medicine, Khyber Teaching Hospital, Peshawar, Pakistan

Usman Saeed Department of Medicine, Khyber Teaching Hospital, Peshawar, Pakistan

Abstract

This report describes a patient who presented with pancoast syndrome, secondary to spindle cell sarcoma of the lung. A 56-year man presented with dyspnea, engorged neck veins and bilateral upper limb pitting edema. The patient also had ptosis and miosis in the right eye. Right ulnar nerve palsy with atrophy of hand muscles was seen. His chest X-ray showed bilateral pleural effusion with an opacity involving the apex of the right lung along with mediastinal widening. Echocardiography revealed a pericardial effusion which was drained. The patient's CT scan of chest strongly suspected a malignant mass in right upper lobe with extensive mediastinal lymphadenopathy, pleural metastases and pericardial involvement. He was started on oxygen inhalation, dexamethasone, and clopidogrel. Bronchoscopic biopsy confirmed the diagnosis of spindle cell sarcoma. Meanwhile, he was advised radiotherapy. The tumour was not amenable to surgery. Spindle cell sarcoma is a rare connective tissue tumor that replicates rapidly. To the best of the authors' knowledge, it is hereby reported the first case of spindle cell sarcoma of the lung presenting as Pancoast syndrome.

Publication Details

Page(s) 623-625

DOI DOI not available

Published Journal: Journal of College of Physicians and Surgeons--Pakistan : JCPSP, Volume: 26, Issue: 7, Year: 2016

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Keywords

Spindle cell sarcoma. Radiotherapy. Pancoast syndrome.

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