Objectives: To study the different clinical presentations and treatment options of extra nodal lymphoma. Design: Prospective Setting & Period: Surgical Unit, Bhawal Victoria Hospital, Bahawalpur from May 01, 2000 to April 30,2004. Material & Methods: Patients of either sex & age diagnosed as case of extra nodal lymphoma were included in the study. The clinical record of the patients included biodata, symptoms & signs, biopsy report, biochemical & radiology report, treatment (surgery, chemotherapy, radiotherapy) given and follow up. Results: In this study we had 13 patients. Out of these 4(31 %) were female and 9(69%) were male. Extra nodal sites included GIT (54%), testis (15%) spinal cord (15%) & skin (15%). The prognosis in most of the cases was not so good. Conclusion: Due to this extensive presence of lymphatic tissue, lymphoma can develop in and spread to, almost any part of the body, For the treatment purpose staging of the disease is very important like any cancer, the earlier the lymphoma is diagnosed, the easier it is to treat.