Pseudoxanthoma elasticum

Arfan ul Bari; Tariq Mehmood

Author(s)

Arfan ul Bari Department of Dermatology, PAF Hospital, Sargodha/Pak Field Hospital-IV, UNAMSIL, Kenema, Sierra Leone (West Africa).

Tariq Mehmood Department of Medicine, Pak Field Hospital-IV, UNAMSIL; Kenema, Sierra Leone'(West Africa).

Abstract

Pseudoxanthoma elasticum is an inherited disorder of connective tissue that is associated with numerous systemic manifestations including various'Cardiovascular abnormalities. We present a case of a 35 years old lady who presented with abnormal wrinkling, pigmentation and laxity of skin. She also had hypertension, peripheral vascular disease, angioid streaks and mitral valve prolapse. She was thoroughly investigated and managed accordingly. She was also educated to minimize the potential risks involved and advised regular follow-up.

Publication Details

Page(s) 650-652

DOI DOI not available

Published Journal: Journal of College of Physicians and Surgeons--Pakistan : JCPSP, Volume: 15, Issue: 10, Year: 2005

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Keywords

Pseudoxanthoma elasticum. Angioid streaks. Skin pigmentation. Mitral valve prolapse. Peripheral vascular disease.

References

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