Acute cardiomyopathy and multiorgan failure in a patient with heochromocytoma and neurofibromatosis type 1. | [Journal of Pakistan Medical Association • 2014]

Author(s):

1. Rezwan Ahmed: Joan C. Edwards School of Medicine, Marshall University, Huntington, WV

2. Yousef Darrat: Department of Cardiovascular Services, Joan C. Edwards School of Medicine, Marshall University, Huntington, WV, USA

3. Eyad Hamoudeh: Department of Endocrinology, Sun City, Arizona, United States

4. Mehair Omar Elhamdani: Department of Cardiovascular Services, Joan C. Edwards School of Medicine, Marshall University, Huntington, WV, USA

5. Abid Yaqub: Department of Medicine, Joan C. Edwards School of Medicine, Marshall University, Huntington, West Virginia, USA

Abstract:

Pheochromocytomas are catecholamine secreting tumours of the adrenal gland, discovered in 0.1% of patients with hypertension. Our case highlights an atypical presentation of heochromocytoma in a patient with Neurofibromatosis type 1 who developoed cardiogenic shock with multi-organ failure. The patient demonstrated reversible dilated cardiomyopathy during her hospital stay, and her blood pressure fluctuated widely. Discovery of right adrenal mass followed by biochemical testing facilitated the diagnosis. Judicious medical management led to an uneventful surgical removal of the tumour followed by marked stabilization of her blood pressure. We discuss the characteristics of heochromocytoma associated with Neurofibromatosis type 1 via reversible cardiac dysfunction.

Page(s): 214-216

DOI: DOI not available

Published: Journal: Journal of Pakistan Medical Association, Volume: 64, Issue: 2, Year: 2014

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