Total colonic aganglionosis in a case of anorectal malformation: A case report | [Journal of Neonatal Surgery • 2022]

Author(s):

1. Rajat Piplani: Department of Pediatric Surgery, All India Institute of Medical sciences, Rishikesh

2. Deepak Kumar Garnaik: Department of Pediatric Surgery, All India Institute of Medical sciences, Rishikesh

3. Shreya Tomar: Department of Pediatric Surgery, All India Institute of Medical sciences, Rishikesh

4. Prashant Kothari: Department of Pediatric Surgery, All India Institute of Medical sciences, Rishikesh

Abstract:

Background: Hirschsprung’s disease (HD) rarely co-occurs with anorectal malformation (ARM). If it occurs, the classical variety of HD is mostly associated. Total Colonic Aganglionosis (TCA) in a case with ARM is exceedingly rare. Case Presentation: A 3-day-old female neonate presented with neonatal intestinal obstruction. of such a rare association. Examination revealed a perineal fistula. A colostomy was formed for persistent abdominal distension, but it did not work properly. Re-exploration revealed TCA with a transition zone at the level of the terminal ileum. Conclusion: Though ARM is associated with several anomalies of various body systems, its association with TCA is exceedingly rare.

Page(s): 1-37

DOI: 10.47338/jns.v11.1100

Published: Journal: Journal of Neonatal Surgery, Volume: 11, Issue: 1, Year: 2022

Keywords:

Hirschsprungs disease , Anorectal Malformation , Total colonic Aganglionosis , Long segment

References:

References are not available for this document.

Citations

Citations are not available for this document.

Citations

Downloads

Views