Epidermodysplasia verruciformis: a rare case presentation | [Journal of Pakistan Association of Dermatologists • 2017]

Author(s):

1. Kumar Prateek: Department of Dermatology, Venereology & Leprosy, Rajendra Institute of Medical Sciences, Ranchi, Jharkhand, India

2. Shyam Sundar Chaudhary: Department of Dermatology, Venereology & Leprosy, Rajendra Institute of Medical Sciences, Ranchi, Jharkhand, India

3. Sonal Sachan: Department of Dermatology, Venereology & Leprosy, Rajendra Institute of Medical Sciences, Ranchi, Jharkhand, India

4. Yuvraj Sahu: Department of Dermatology, Venereology & Leprosy, Rajendra Institute of Medical Sciences, Ranchi, Jharkhand, India

5. Pooja Choubey: Department of Dermatology, Venereology & Leprosy, Rajendra Institute of Medical Sciences, Ranchi, Jharkhand, India

Abstract:

Epidermodysplasia verruciformis (EV) is a rare genodermatosis characterized by a unique susceptibility to cutaneous infection by a group of phylogenetically related human papilloma viruses (HPVs). These patients show a defect in cell-mediated immunity specific toward the causative HPVs that leads to lifelong disease. The defect is usually inherited as autosomal recessive trait and presents clinically with plane warts, pityriasis versicolor-like lesions and reddish verrucous plaques. Dysplastic and malignant changes in the form of actinic keratoses, Bowen's disease and squamous cell carcinoma (SCC) are common but metastasis occurs rarely. A totally effective treatment against EV is as yet highly desirable. We report a case of EDV in a 13-year-old female patient with confluent wart like lesions, pityriasis versicolor like lesions and reddish plaques. The case is being reported in view of rarity of disease.

Page(s): 92-94

DOI: DOI not available

Published: Journal: Journal of Pakistan Association of Dermatologists, Volume: 27, Issue: 1, Year: 2017

Keywords:

human papilloma virus , Epidermodysplasia verruciformis

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