Vanishing gastroschisis with jejunal atresia and extreme short bowel syndrome: A case series | [Journal of Neonatal Surgery • 2021]

Author(s):

1. Naresh Pawar: College,302004,India -Department of Pediatric Surgery, SMS Medical College,Jaipur, Rajasthan,India

2. Pramila Sharma: Department of Pediatric Surgery, SMS Medical College, Jaipur, Rajasthan, India

3. Punit Singh Parihar: Department of Pediatric Surgery, SMS Medical College, Jaipur, Rajasthan, India

4. Manika Boipai: Department of Pediatric Surgery, SMS Medical College, Jaipur, Rajasthan, India

Abstract:

Background: Vanishing gastroschisis may occur due to spontaneous partial or complete clo-sure of anterior abdominal wall defect around the viscera, leading to small bowel ischemia and resultant entry/exit level atresia and extremely short length of the remaining bowel. The prognosis is very poor, even after aggressive surgery, and requires prolonged total parenteral nutrition. Case Series: We report two female neonates, one with closed and another with closing vanish-ing gastroschisis, associated with jejunal atresia and extreme short bowel syndrome. In both patients, the antenatal scans showed gastroschisis without the evidence of vanishing gas-troschisis. In both neonates, palliative surgeries were done. Both patients died after a few days due to short bowel syndrome and sepsis. Conclusion: When antenatally detected gastroschisis presents with closed or closing anterior abdominal wall defect, (vanishing gastroschisis), the parents/caregivers must be counseled about the poor prognosis of this condition. A tailored approach to either palliation or aggres-sive therapy is essential in this rare condition.

Page(s): 1-7

DOI: 10.47338/jns.v10.932

Published: Journal: Journal of Neonatal Surgery, Volume: 10, Issue: 1, Year: 2021

Keywords:

Jejunal atresia , Extreme short bowel syndrome , Vanishing gastroschisis

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