Tension Pneumoperitoneum: a Rare Presentation of Megacystis Microcolon Intestinal Hypoperistalsis Syndrome. | [Journal of Ayub Medical College • 2019]

Author(s):

1. Farheen Raza: Department of Radiology, Shifa International Hospital, Islamabad, Pakistan

2. Maham Jehangir: Department of Radiology, Shifa International Hospital, Islamabad, Pakistan

3. Rashed Nazir: Department of Radiology, Shifa International Hospital, Islamabad, Pakistan

4. Nasir Aziz Khan: Department of Radiology, Shifa International Hospital, Islamabad, Pakistan

Abstract:

Megacystis microcolon intestinal hypoperistalsis syndrome also known as Berdon syndrome is characterized by enlarged urinary bladder, small colon and reduced or absent intestinal peristalsis. We report a case of 4 days old female suffering from MMIHS presenting with tension pneumoperitoneum. To the best of our knowledge, this is the first reported case of MMIHS, having this unusual presentation.

Page(s): 136-137

DOI: DOI not available

Published: Journal: Journal of Ayub Medical College, Volume: 31, Issue: 1, Year: 2019

Keywords:

Keywords are not available for this article.

References:

[1] BerdonWE,BakerDH,BlancWA,GayB,SantuliTV,DonovanC, 1976.Megacystis-microcolon-intestinal hypoperistalsis syndrome: a new cause of intestinal obstruction in the newborn - Report of radiological findings in five newborn girls,AM J Roentgenol 126 957 -64

[2] AnnerenG,MeurlingS, 1991.Megacystis-microcolonintestinal hypoperistalsis syndrome (MMIHS): an autosomal recessive disorder - Clinical reports and review of the literature,Am J Med Genet 41 251 -4

[3] VerbruggenSC,WijnenRM, 2004.Megacystis microcolon-intestinal hypoperistalsis syndrome: a case report,J Matern Fetal Neonatal Med 16 140 -1

[4] ManopJ,ChamnanvanakijS,WattanasarnC, 2004.Megacystis Microcolon Intestinal Hypoperistalsis Syndrome (MMIHS): A Case Report in Thailand,J Med Assoc Thai 87 1385 -8

[5] 1983.Megacystis-microcolon-intestinal hypoperistalsis syndrome: a visceral myopathy,J Pediatr Surg 18 64 -9

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