Adult-onset erythrokeratodermia variabilis (EKV) triggered by pregnancy and crash dieting: A rare case report | [Journal of Pakistan Medical Association • 2024]

Author(s):

1. Ghazal Afzal: PNS Shifa Hospital, Karachi, Pakistan

2. Najia Ahmed: Department of Dermatology, PNS Shifa Hospital, Karachi, Pakistan

3. Nighat Jamal: Department of Histopathology, PNS Shifa Hospital, Karachi, Pakistan

4. Fatima Zahoor: Department of Dermatology, PNS Shifa Hospital, Karachi, Pakistan

Abstract:

Erythrokeratodermia variabilis (EKV) is a rare inherited genodermatosis characterised by migratory and erythematous patches changing over the course of hours to days and fixed keratotic plaques. The disease begins mostly at birth or within the first year of life; it very rarely starts after childhood. We present here a sporadic case with adult onset EKV that was aggravated by pregnancy with spontaneous resolution, and later on, after crash diet more persistent patches and plaques appeared with no spontaneous resolution. The patient showed excellent response to systemic retinoids.

Page(s): 1687-1689

DOI: 10.47391/JPMA.9785

Published: Journal: Journal of Pakistan Medical Association, Volume: 74, Issue: 9, Year: 2024

Keywords:

Pregnancy , sporadic , adult onset , Acitretin , Crash Diet , retinoids , Erythrokeratodermia variabilis

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